Tricuspid Atresia—Child

(Single Ventricle Defect—Child)
  • Definition

    Tricuspid atresia is an abnormal development of the right side of the heart. It includes a missing valve between the upper and lower chamber and a smaller than normal lower chamber. Tricuspid atresia can make it difficult for your heart to efficiently pump blood to the lungs to get oxygen. Some may also have holes in the wall between the left and right side of the heart. The holes allow oxygen-rich and oxygen-poor blood to mix.
    Heart Chambers and Valves
    heart anatomy
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    Blood Flow Through the Heart
    IMAGE
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  • Causes

    Tricuspid atresia develops when the baby is in the womb. It is not known exactly why some hearts develop this way.
  • Risk Factors

    Factors that increase the risk for congenital heart defects like tricuspid atresia include:
    • Family history of congenital heart defect
    • Chromosomal disorder such as Down syndrome
    • Previous pregnancy with fetal heart abnormalities or miscarriage
    • Conditions during pregnancy, such as:
      • Being infected with a virus
      • Having poorly controlled diabetes
      • Drinking alcohol
      • Taking certain medications
  • Symptoms

    Symptoms may include:
    • Blue or pale grayish skin color
    • Fast breathing
    • Sweating
    • Poor feeding/poor weight gain
    • Fatigue
  • Diagnosis

    Tricuspid atresia may be diagnosed before birth.
    After birth, a tricuspid atresia may be suspected if the baby has a blue-ish color and a heart murmur is detected during a physical exam.
    Images may be taken of your baby's bodily structures. This can be done with:
    Your child's heart function may be tested. This can be done with:
  • Treatment

    Treatment is important to prevent severe complications such as heart failure . Treatments may include:
    Medication
    Medication may be given to:
    • Improve the levels of oxygen in the blood.
    • Manage the level of fluids in the body to decrease workload on the heart.
    Oxygen may also be given to increase the amount of oxygen in the blood.
    Surgery
    Surgery is often needed right away. Follow-up surgeries may also be needed at ages 3-6 months and 2-5 years.
    The goal of surgery is to:
    • Improve blood flow within the heart
    • Restore connections between the heart, lungs, and body
    The exact surgery will depend on the type and severity of defects that are present. For example, a shunt may be placed to increase blood flow to the lungs. Later, a series of surgeries will be done to reroute blood flow through the heart, lungs, and body.
    Lifelong Monitoring
    Your child will have regular exams from a heart specialist. Your child may also need antibiotics before certain medical or dental procedures to prevent a heart infection.
  • Prevention

    Preventing fetal heart defects may not always be possible. Good prenatal care may reduce some type of congenital heart defects. Prenatal care includes:
    • Visiting the doctor regularly to monitor your health and the health of the baby
    • Eating nutritious food and taking prenatal vitamins
    • Avoiding alcohol, smoking , and using drugs during pregnancy
    • Practicing good hygiene and staying away from people who are sick
  • RESOURCES

    American Heart Association http://www.heart.org

    Family Doctor—American Academy of Family Physicians http://familydoctor.org

    CANADIAN RESOURCES

    Canadian Cardiovascular Society http://www.ccs.ca

    Heart and Stroke Foundation of Canada http://www.heartandstroke.com

    References

    Tricuspid atresia. Boston Children’s Hospital website. Available at: http://www.childrenshospital.org/az/Site508/mainpageS508P0.html. Accessed November 10, 2014.

    Tricuspid atresia. Children’s Hospital of Philadelphia website. Available at: http://www.chop.edu/service/cardiac-center/heart-conditions/tricuspid-atresia.html. Accessed November 10, 2014.

    Tricuspid atresia. EBSCO DynaMed website. Available at:  http://www.ebscohost.com/dynamed. Updated October 14, 2014. Accessed November 10, 2014.

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